Hemophilia
- Bleeding into joints
- Hematomas
- Ecchymosis
- Hematuria
- Hematemesis
- Epistaxis
- Bleeding gums
- Easy Bruising
- Â Prolonged bleeding after cuts/surgery
Hemophilia
Hemophilia
A group of genetic disorder that affect the body’s ability to properly clot blood (bleeding/bruising). Two main types of hemophilia, type A and type B, which are caused by deficiencies in clotting factor VIII and IX, respectively.
Treatment
Replacement of clotting factors VIII or IX, antifibrinolytics, and desmopressin (DDAVP)
Nursing interventions
- Bleeding precautions
- Administration of replacements factors
- Administer desmopressin which increases factor VIII and von Willebrand factorÂ
- Monitor for joint pain: immobilize affected joint, elevate, and apply ice
- Pressure to bleeding sites x 15 minutes
- Assess neurological status (brain bleed)
- Avoid contact sports; wear protective devices such as helmets and elbow pads.
- wear Medic-Alert bracelet.
- Labs: Normal PT, prolonged PTT, prolonged bleeding time, and normal platelets
