Hemophilia

Hemophilia

A group of genetic disorder that affect the body’s ability to properly clot blood (bleeding/bruising). Two main types of hemophilia, type A and type B, which are caused by deficiencies in clotting factor VIII and IX, respectively.

Hemophilia

  • Bleeding into joints
  • Hematomas
  • Ecchymosis
  • Hematuria
  • Hematemesis
  • Epistaxis
  • Bleeding gums
  • Easy Bruising
  •  Prolonged bleeding after cuts/surgery

Treatment

Replacement of clotting factors VIII or IX, antifibrinolytics, and desmopressin (DDAVP)

Nursing interventions

  • Bleeding precautions
  • Administration of replacements factors
  • Administer desmopressin which increases factor VIII and von Willebrand factor 
  • Monitor for joint pain: immobilize affected joint, elevate, and apply ice
  • Pressure to bleeding sites x 15 minutes
  • Assess neurological status (brain bleed)
  • Avoid contact sports; wear protective devices such as helmets and elbow pads.
  • wear Medic-Alert bracelet.
  • Labs: Normal PT, prolonged PTT, prolonged bleeding time, and normal platelets
Immobilize swollen, tender with limited ROM joints
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