A group of genetic disorder that affect the body’s ability to properly clot blood (bleeding/bruising). Two main types of hemophilia, type A and type B, which are caused by deficiencies in clotting factor VIII and IX, respectively.
Hemophilia
Bleeding into joints
Hematomas
Ecchymosis
Hematuria
Hematemesis
Epistaxis
Bleeding gums
Easy Bruising
 Prolonged bleeding after cuts/surgery
Treatment
Replacement of clotting factors VIII or IX, antifibrinolytics, and desmopressin (DDAVP)
Nursing interventions
Bleeding precautions
Administration of replacements factors
Administer desmopressin which increases factor VIII and von Willebrand factorÂ
Monitor for joint pain: immobilize affected joint, elevate, and apply ice
Pressure to bleeding sites x 15 minutes
Assess neurological status (brain bleed)
Avoid contact sports; wear protective devices such as helmets and elbow pads.
wear Medic-Alert bracelet.
Labs: Normal PT, prolonged PTT, prolonged bleeding time, and normal platelets
Immobilize swollen, tender with limited ROM joints